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Optic Nerve Hypoplasia

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Optic Nerve Hypoplasia (ONH)

Optic Nerve Hyoplasia (ONH) results is an underdevelopment of optic nerve (the part of the brain that transmits information from the eye to the brain). Over 80% of people with bilateral ONH also have hypopituitarism or hypothalamic dysfunction. This dysfunction presents huge challenges in for the body’s ability to regulate the internal physiological mechanisms controlling behavior and pituitary gland functioning. Areas of concern include:

1.     Thirst and hunger: feeding behaviors including overeating with obesity, poor eating with wasting, and aversion to certain food textures.

2.     Water seeking behavior: which may be mistaken for diabetes insipidus.

3.     Sleep: biological clock, may have loss of rhythmicity and sleep or wakefulness, may cause disruption to family life (circadian rhythms)

4.     Temperature regulation: body temperature regulation and frequently hospitalized to rule out sepsis

5.     May have obsessive–compulsive behavior, auditory and tactile defensiveness.

6.     The need for rigid routines

7.     Gross and fine motor skills, speech and interacting with people.

ONH Websites & Resources: 

·        A Unique Way of Learning: Teaching Young Children with Optic Nerve Hypoplasia is an excellent resource that costs $10.00 and is available through the IESBVI Media Center and TVI/O&M.

·         One Small Voice Foundation includes a nice resource for parents teams Optic Nerve Hypoplasia: A Guide for Parents

·         Children’s Hospital Los Angeles Optic Nerve Hypoplasia

·        Optic Nerve Hypoplasia (ONH): The Spectrum with a Practical Approach this article provides a nice summary and includes helpful statistics/recommendations.


Kind of like this Blog on ONH http://paintsandpistols.blogspot.com/2014/04/what-is-optic-nerve-hypoplasia_13.html?m=1

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